Dental anomalies in primary teeth may affect permanent teeth eruption and occlusion disability. Dental anomalies occurrences such as fusion in primary dentition can be frequent in daily practice. The aim of this study is to present a case of fusion, the clinical management, and the consequent effects. The paper presents a case of the fused primary mandibular lateral incisor and primary canine along with agenesis of the permanent lateral incisor. Keywords- Primary teeth fusion, Agenesis